Defining Characteristics
Red line along gingivial sulcus (white picket fence), no scarring.
Disease Development
Autoimmune blistering disorder where antibodies are directed at hemidesmosomes (sub-basal) so loss of epidermal attachment to basement membrane
Potential Causes
Autoantibodies against BPAG2, laminins, integrins
Lab/Imaging
Histology? Subepidermal blister (white space btwn epidermis & dermis) (sub-basal split), healthy epidermis, +eosinophils (pink)
Dx confirmed w/ immunofluorescent Abs
Prevention
Oral form of Mucus Membrane Pemphigoid has better prognosis (very little scarring)