Types
Sunburn
,
Albinism
,
Vitiligo
,
Viral Hepatitis
,
Epidermolysis bullosa (EB)
,
General
,
EB Simplex
,
Junctional
,
Dystrophic (Recessive-RDEB or Dominant- DDEB)
,
Epidermolysis bullosa acquisita
,
Bullous pemphigoid
,
Mucus membrane pemphigoid
,
Ocular cicatricial pemphigoid
,
Pemphigus vulgaris
,
Pemphigus foliaceus
,
General
,
Acute dermatitis (eczema)
,
Chronic dermatitis
,
Subacute dermatitis
,
Atopic Dermatitis (AD)
,
Stasis Dermatitis (SD)
,
Lichen Simplex Chronicus (LSC)
,
Contact Dermatitis - Irritant
,
Contact Dermatitis - Allergic (ACD)
,
Seborrheic Dermatitis
,
Bacterial folliculitis
,
Hot tub folliculitis
,
Verruca vulgaris
,
Verruca plantaris
,
Condylomata acuminata
,
Filiform warts
,
Verruca plana
,
Sclerosteosis
,
Van Buchem
,
Worth type
,
Acute
,
Chronic
,
Hematogenous
,
Contiguous
,
Acute bacterial
,
Chronic septic arthritis
,
Disseminated gonococcial infection (DGI)
,
Early (<3m after surgery)
,
Delayed (3-24m)
,
Late (>2y)
,
Classical
,
Hypermobility
,
Arthrochalasia
,
Vascular
,
Dermatosparaxis
,
Kyphoscoliosis
,
Duchenne MD
,
Becker's MD
,
Myotonic dystrophy type I
,
Acute
,
Chronic
,
Monomicrobial
,
Polymicrobial
,
Giant Melanocytic Nevus
,
Polyostotic Monostotic
,
Autosomal recessive infantile malignant (ARO)
,
Autosomal dominant (Albers-Schonberg) (ARO)
,
Camurati-Engelmann
,
Benign
,
Benign
,
Benign
,
McArdle's disease
,
Carnitine palmitoyltransferase II deficiency
,
Mitochondrial myopathy
,
Dermatomyositis
,
Polymyositis
,
Inclusion body myopathy
,
Soft tissue pain disorder
,
Episodic monoarticular Polyarticular Tophaceous gout
,
Central core disease
,
Basal Cell Nevus Syndrome (BCNS)
,
Xeroderma pigmentosum (XP)
,
Sun tan
,
Ichthyosis
,
Psoriasis
,
Ectodermal Dysplasia
,
Keloid
,
Acne
,
Tinea versicolor
,
Molluscum Contagiosum
,
Varicella Zoster Virus (VZV) (Shingles)
,
Scabies
,
Eryisipelas
,
Gas gangrene (myonecrosis)
,
Osteoporosis
,
Pycnodysostosis
,
Carbonic Anhydrase II deficiency
,
Fibrodysplasia ossificans progressive (FOP)
,
Marfan Syndrome
,
Stickler Syndrome
,
Achondroplasia
,
Polymyalgia Rheumatica (PR)
Disease Overview
A Pemphigus is a skin disease in which watery blisters form under the skin.
Defining Characteristics
Inter-epidermal blisters, jagged & flaccid blisters w/ positive Nikolsky sign (easy to deform w/ slight pressure), hyperpigmentation in healing areas, not too much scarring, severe nail disease, oral lesions
Epidemiology
N/A
Risk factors
N/A
Lab/Imaging
Histology? Basal epidermis still attached to BM, and rete ridges still visible but huge white space above represents blister (suprabasal split)
Chicken wire appearance w/ direct immunofluorescence
Chicken wire appearance w/ direct immunofluorescence
Conventional Treatment
Immunosuppressants, corticosteroids; new therapies (tyrosine kinase inhibitors to increase resistance to pemphigus IgG)
Complications
side effects of steroids; high fatality w/o tx